目的

探讨额-眶骨纤维异常增殖症的手术方法，评价视神经管减压+计算机塑形钛网颅骨缺损修补术的手术疗效。

方法

回顾性分析青岛疗养院眼科2005至2013年收治的25例纤维异常增殖症患者的临床资料，并进行统计学分析。

结果

随访1～9 年，13 例患者病变呈自限性倾向，无明显进展，1例患者额颞部凸面隆起加重但视力仍未受影响；2例随访患者患眼视力逐渐减退，改行手术治疗视力改善，9例手术患者10只视力受影响的眼中4只视力改善，患者面容皆明显改观，效果满意。全部手术病例的病变骨质病理学检查结果均为骨纤维结构不良。

结论

累及额-眶的骨纤维异常增殖症伴视力下降的患者，行病变骨切除+保留眶壁骨皮质患侧视神经管减压+计算机塑形钛网颅骨缺损修补术，可有效防止视力下降，减少并发症。

Objective

To investigate the operation method of the patients with fronto-orbital fibrous dysplasia and to evaluate the curative effects of optic canal decompression and cranioplasty by computer shaping titanium mesh.

Methods

The clinical data of 25 patients with fronto-orbital fibrous dysplasia who were treated in the Department of Ophthalmology of Qingdao Sanatorium of Shandong Province from 2005 to 2013 were retrospectively analyzed.

Results

Patients were followed up for 1～9 years, 13 cases have self limiting tendency without significant progress, 1 case with frontotemporal convex uplift increased without affected the vision, 2 cases were treated by operation after the visual decreased, 4 of 10 eyes of 9 cases the visual improved, all of them with face significantly improved were satisfied. The pathological examination results showed all bone lesions were bone fibrous dysplasia.

Conclusions

Patients underwent pathological bone resection and retained orbital wall bone cortex optic canal decompression and cranioplasty by computer shaping titanium mesh with fibrous dysplasia involving the fronto-orbital with vision decreased can effectively prevent vision loss and reduce complications.