Treatment strategies of neurofibromatosis type Ⅱ

doi:10.3877/cma.j.issn.2095-9141.2017.02.013

Abstract

Abstract:

Neurofibromatosis is an autosomal dominant disorder caused by abnormal differentiation of neural crest cells, which often involves the nerve, muscle, bone, internal organs and skin. Neurofibromatosis is a congenital development benign disease, according to its clinical characteristics and responsibilities gene of different type can be divided into type I (NF1) and Ⅱ (NF2) two types. Compared with type I, neurofibromatosis type Ⅱ has a lower incidence of neurofibromatosis. About 3/10 of all patients with vestibular nerve schwann cell tumor and other tumours, including meningiomas, ependymoma and astrocytoma and peripheral nerve schwann cell tumor. Many patients also can appear capsule opacity.

Key words: Pathogenesis, Heredity, Tumour

Lihua Chen, Ruxiang Xu. Treatment strategies of neurofibromatosis type Ⅱ[J]. Chinese Journal of Neurotraumatic Surgery(Electronic Edition), 2017, 03(02): 114-118.

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